L-Phenylalanine CAS: 63-91-2 99% funfun lulú
| Nọmba katalogi | XD90317 |
| Orukọ ọja | L-Cysteine hydrochloride anhydrous |
| CAS | 63-91-2 |
| Ilana molikula | C9H11NO2 |
| Òṣuwọn Molikula | 165.19 |
| Awọn alaye ipamọ | Ibaramu |
| Ti irẹpọ Owo idiyele koodu | 29224985 |
Ọja Specification
| Ifarahan | Funfun okuta lulú |
| Ayẹwo | 99% |
| Yiyi pato | -20.4 si -35.2 |
| Awọn irin ti o wuwo | <0.002% |
| Asiwaju | <10mg/kg |
| pH | 5.4 - 6 |
| Isonu lori Gbigbe | <0.40% |
| Aloku lori Iginisonu | <0.10% |
Ninu arun ito omi ṣuga oyinbo maple (MSUD), L-amino (BCAA) ti o ni ẹka ati awọn acids 2-oxo (BCOA) kojọpọ ninu awọn omi ara nitori aipe ajogunba ti eka-pq 2-oxo acid dehydrogenase eka iṣẹ.Ni MSUD, alaye diẹ wa lori pataki ti ito nu ti awọn agbo-ẹwọn-ẹka.A ṣe ayẹwo imukuro kidirin ti leucine, valine, isoleucine ati alloisoleucine, ati awọn 2-oxo acids ti o baamu 4-methyl-2-oxopentanoate (KIC), 3-methyl-2-oxobutanoate (KIV), (S) (S- KMV), ati (R) -3-methyl-2-oxopentanoate (R-KMV), ni lilo awọn orisii pilasima ati awọn ayẹwo ito (n = 63) lati ọdọ awọn alaisan 10 pẹlu MSUD kilasika.Iyọkuro kidirin ida ti BCAA ọfẹ wa ni iwọn deede (<0.5%) ati ominira ti awọn ifọkansi pilasima.Iyọkuro ti didi (N-acylated) BCAA jẹ deede ati pe ko dale ni pataki lori awọn ifọkansi pilasima BCAA.Iyọkuro kidirin ida ti BCOA wa ni aṣẹ KIC << KIV
